Title

Early childhood onset of high-grade atrioventricular block in Hunter syndrome.

Document Type

Article

Publication Date

5-2018

Identifier

DOI: 10.1017/S1047951118000215

Abstract

Cardiac involvement has been reported in various mucopolysaccharidoses syndromes. Cardiac valve pathology is the most prominent cardiac manifestation of patients with these syndromes. To date, there have been no reports of early childhood onset of high-grade atrioventricular block in patients with Hunter syndrome. We present a case of a 3-year-old boy with Hunter syndrome who was found to have various degrees of atrioventricular block. This case highlights the importance of early routine cardiac screening for conduction abnormalities and close follow-up in patients with mucopolysaccharidoses syndromes.

Journal Title

Cardiology in the young

Volume

28

Issue

5

First Page

786

Last Page

787

MeSH Keywords

Atrioventricular Block; Cardiac Pacing, Artificial; Child, Preschool; Electrocardiography; Follow-Up Studies; Humans; Male; Mucopolysaccharidosis II; Telemetry; Time Factors

Keywords

Children; Hunter syndrome; atrioventricular block; electrophysiology (EP)

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