Repair of "simple" total anomalous pulmonary venous connection: a review from the Pediatric Cardiac Care Consortium.

Creator(s)

James D. St Louis
Brian A. Harvey
Jeremiah S. Menk
Geetha Raghuveer, Children's Mercy HospitalFollow
James E. O'Brien, Children's Mercy HospitalFollow
Roosevelt Bryant
Lazaros Kochilas

Document Type

Article

Publication Date

7-2012

Identifier

DOI: 10.1016/j.athoracsur.2012.03.006; PMCID: PMC4365445

Abstract

BACKGROUND: Outcomes for repair of total anomalous pulmonary venous connection (TAPVC) from individual institutions suggest a significant improvement in mortality over the past several decades. The purpose of this study is to review the outcomes after repair of TAPVC from a large multiinstitutional registry.

METHODS: A retrospective review of the multiinstitutional database, the Pediatric Cardiac Care Consortium (PCCC), was used to identify patients with the diagnosis of TAPVC who underwent complete correction between 1982 and 2007. Data reviewed included age, decade of primary operation, anatomic type, presentation, and in-hospital mortality.

RESULTS: Of the 118,084 surgical procedures submitted to the PCCC, 2,191 (1.9%) consisted of primary surgical correction of TAPVC. Sixty-one percent of the cohort was male, with 6.8% reported as premature. Overall in-hospital surgical mortality for simple TAPVC was 13%. Mortality was 20% from 1982 to 1989, 16% from 1990 to 1999, and 8% from 2000 to 2007. Obstruction to the anomalous pulmonary venous connection occurred in 29%, with a mortality of 26%.

CONCLUSIONS: Surgical outcomes from repair of congenital cardiac anomalies have significantly improved over the past several decades. Multiinstitutional large databases are needed to confirm results published from single-institution experiences. Although improvements in surgical repair of TAPVC have occurred over the past three decades, specific subtypes still experience significant mortality.

Journal Title

The Annals of thoracic surgery

Volume

94

Issue

1

First Page

133

Last Page

137

MeSH Keywords

Adolescent; Child; Child, Preschool; Female; Hospital Mortality; Humans; Infant; Infant, Newborn; Male; Pulmonary Veins; Retrospective Studies

Keywords

Hospital Mortality; Pulmonary Veins; Retrospective Studies

Comments

Grant support

• UL1 RR033183/RR/NCRR NIH HHS/United States
• UL1 TR000114/TR/NCATS NIH HHS/United States

Recommended Citation

St Louis, J. D., Harvey, B. A., Menk, J. S., Raghuveer, G., O'Brien, J. E., Bryant, R., Kochilas, L. Repair of "simple" total anomalous pulmonary venous connection: a review from the Pediatric Cardiac Care Consortium. The Annals of thoracic surgery 94, 133-137 (2012).