Document Type

Article

Publication Date

1-2019

Identifier

DOI: 10.1055/s-0039-3399557; PMCID: PMC6938457

Abstract

Osteogenesis imperfecta (OI) is a genetic disorder of collagen resulting in a "fragile" skeleton with increased fracture risk and other complications, dependent on the specific variant. Pectus deformities of the chest wall, while not common, can be associated with OI. The use of a pectus carinatum brace in a patient with OI poses unknown risks for fractures and adverse treatment outcomes. We successfully applied external compression bracing using the dynamic compression system to one such patient. This case illustrates the ability to treat an OI patient with pectus carinatum using a nonsurgical brace, without complications, resulting in an excellent cosmetic result.

Journal Title

European J Pediatr Surg Rep

Volume

7

Issue

1

First Page

117

Last Page

120

Keywords

dynamic compression system; osteogenesis imperfecta; pectus carinatum

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