Title

Pial Synangiosis Ameliorates Movement Disorders in the Absence of Prior Stroke in Moyamoya Disease.

Document Type

Article

Publication Date

4-1-2016

Identifier

DOI: 10.1177/0883073815609152

Abstract

BACKGROUND: Moyamoya disease is a rare cerebrovascular disease characterized by progressive stenosis of the bilateral distal internal carotid arteries and their proximal branches. Both chorea and dystonia have been reported as the initial presentation of moyamoya disease.

OBJECTIVE: The objective was to define the clinical presentation and describe the disease course following pial synangiosis of 3 patients with dyskinesias.

METHODS: A retrospective chart review of 3 cases of patients presenting with movement disorders and ultimately diagnosed with moyamoya disease was performed.

RESULTS: The authors present a case series of 1 patient with dystonia and 2 patients with chorea, all diagnosed with moyamoya disease. All patients experienced resolution of their movement disorders following pial synangiosis. Magnetic resonance imaging disclosed moyamoya disease-related basal ganglia anomalies in all patients.

CONCLUSIONS: Moyamoya disease is an important and surgically treatable cause of movement disorders.

Journal Title

Journal of child neurology

Volume

31

Issue

5

First Page

646

Last Page

651

MeSH Keywords

Cerebral Angiography; Female; Humans; Imaging, Three-Dimensional; Magnetic Resonance Imaging; Male; Movement Disorders; Moyamoya Disease; Pia Mater; Retrospective Studies; Stroke

Keywords

chorea; dystonia; indirect bypass; movement disorder; moyamoya; pediatric; pial synangiosis

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