Review of surgical and anesthetic management for esophageal atresia with tracheoesophageal fistula, unilateral pulmonary agenesis and dextrocardia.

Creator(s)

Rebecca M. Rentea, Children's Mercy HospitalFollow
Tolulope A. Oyetunji, Children's Mercy HospitalFollow
John Erkmann, Children's Mercy HospitalFollow
Joshua Q. Knowlton, Children's Mercy Hospital
Richard J. Hendrickson, Children's Mercy HospitalFollow

Document Type

Article

Publication Date

7-1-2017

Identifier

DOI: 10.1007/s00383-017-4090-7

Abstract

Association of unilateral severe pulmonary atresia or agenesis and esophageal atresia (EA) with or without tracheoesophageal fistula (TEF) and dextrocardia is a rare and highly lethal combination. We report a case of a full-term female infant who had EA with TEF, right lung agenesis, and dextrocardia. Repair of the fistula took place on day of life 3. We describe anesthetic and surgical concerns of this patient's case which are keys to a good operative outcome as well as follow-up for the patient.

Journal Title

Pediatric surgery international

Volume

33

Issue

7

First Page

817

Last Page

821

MeSH Keywords

Dextrocardia; Esophageal Atresia; Tracheoesophageal Fistula; Lung Agenesis; Surgical Procedures; Operative; Anesthesia

Keywords

Dextrocardia; Esophageal atresia (EA); Lung agenesis; Tracheoesophageal fistula (TEF); Unilateral pulmonary agenesis

Recommended Citation

Rentea RM, Oyetunji TA, Erkmann J, Knowlton JQ, Hendrickson RJ. Review of surgical and anesthetic management for esophageal atresia with tracheoesophageal fistula, unilateral pulmonary agenesis and dextrocardia. Pediatr Surg Int. 2017;33(7):817-821. doi:10.1007/s00383-017-4090-7