Title

Outcomes and Complications in Management of Congenital Myopathy Early-Onset Scoliosis.

Document Type

Article

Publication Date

10-1-2021

Identifier

DOI: 10.1097/BPO.0000000000001922

Abstract

Background: Congenital myopathies (CMs) are complex conditions often associated with early-onset scoliosis (EOS). The purpose of this study was to investigate radiographic outcomes in CM patients undergoing EOS instrumentation as well as complications. Secondarily, we sought to compare these patients to a population with higher prevalence, cerebral palsy (CP) EOS patients.

Methods: This is a retrospective study of a prospectively collected multicenter registry. The registry was queried for EOS patients with growth-sparing instrumentation (vertical expandable prosthetic titanium ribs, magnetically controlled growing rods, traditional growing rod, or Shilla) and a CM or CP diagnosis with minimum 2 years follow-up. Outcomes included major curve magnitude, T1-S1 height, kyphosis, and complications.

Results: Sixteen patients with CM were included. Six (37.5%) children with CM experienced 11 complications by 2 years. Mean major curve magnitude for CM patients was improved postoperatively and maintained at 2 years (P0.05). Ninety-seven patients with CP EOS were included as a comparative cohort. Fewer CP patients required baseline respiratory support compared with CM patients (20.0% vs. 92.9%, P

Conclusions: EOS CM children face a high risk of complication after growing instrumentation, with similar curve correction and risk of complication to CP patients.

Level of evidence: Level III.

Journal Title

Journal of pediatric orthopedics

Volume

41

Issue

9

First Page

531

Last Page

536

MeSH Keywords

Child; Follow-Up Studies; Humans; Kyphosis; Muscular Diseases; Retrospective Studies; Ribs; Scoliosis; Spine; Treatment Outcome

Keywords

Follow-Up Studies; Kyphosis; Muscular Diseases; Retrospective Studies; Ribs; Scoliosis; Spine; Treatment Outcome

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