Orthognathic Correction in Prader-Willi Syndrome: Occlusion and Sleep Restored.
Document Type
Article
Publication Date
3-2019
Identifier
DOI: 10.1177/1055665618775724
Abstract
Children with Prader-Willi Syndrome (PWS) may present with a malocclusion and have a high propensity of developing obstructive sleep apnea (OSA). Obstructive sleep apnea is associated with short- and long-term adverse effects that negatively impact children with PWS. A case of a 15-year-old male with PWS, OSA, and a debilitating malocclusion is presented who underwent a combination of Le Fort 1 osteotomy, genioplasty, and tongue reduction to successfully treat his OSA and malocclusion. In select cases, orthognathic correction and other surgical therapies should be considered in patients with PWS.
Journal Title
The Cleft palate-craniofacial journal : official publication of the American Cleft Palate-Craniofacial Association
Volume
56
Issue
3
First Page
415
Last Page
418
MeSH Keywords
Adolescent; Dental Occlusion; Humans; Male; Polysomnography; Prader-Willi Syndrome; Sleep Apnea, Obstructive
Keywords
OSA; Prader-Willi Syndrome; orthognathic surgery
Recommended Citation
Xiao KK, Tomur S, Beckerman R, Cassidy K, Lypka M. Orthognathic Correction in Prader-Willi Syndrome: Occlusion and Sleep Restored. Cleft Palate Craniofac J. 2019;56(3):415-418. doi:10.1177/1055665618775724