Title

Orthognathic Correction in Prader-Willi Syndrome: Occlusion and Sleep Restored.

Document Type

Article

Publication Date

3-2019

Identifier

DOI: 10.1177/1055665618775724

Abstract

Children with Prader-Willi Syndrome (PWS) may present with a malocclusion and have a high propensity of developing obstructive sleep apnea (OSA). Obstructive sleep apnea is associated with short- and long-term adverse effects that negatively impact children with PWS. A case of a 15-year-old male with PWS, OSA, and a debilitating malocclusion is presented who underwent a combination of Le Fort 1 osteotomy, genioplasty, and tongue reduction to successfully treat his OSA and malocclusion. In select cases, orthognathic correction and other surgical therapies should be considered in patients with PWS.

Journal Title

The Cleft palate-craniofacial journal : official publication of the American Cleft Palate-Craniofacial Association

Volume

56

Issue

3

First Page

415

Last Page

418

MeSH Keywords

Adolescent; Dental Occlusion; Humans; Male; Polysomnography; Prader-Willi Syndrome; Sleep Apnea, Obstructive

Keywords

OSA; Prader-Willi Syndrome; orthognathic surgery

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