Orthognathic Correction in Prader-Willi Syndrome: Occlusion and Sleep Restored.
Children with Prader-Willi Syndrome (PWS) may present with a malocclusion and have a high propensity of developing obstructive sleep apnea (OSA). Obstructive sleep apnea is associated with short- and long-term adverse effects that negatively impact children with PWS. A case of a 15-year-old male with PWS, OSA, and a debilitating malocclusion is presented who underwent a combination of Le Fort 1 osteotomy, genioplasty, and tongue reduction to successfully treat his OSA and malocclusion. In select cases, orthognathic correction and other surgical therapies should be considered in patients with PWS.
The Cleft palate-craniofacial journal : official publication of the American Cleft Palate-Craniofacial Association
Adolescent; Dental Occlusion; Humans; Male; Polysomnography; Prader-Willi Syndrome; Sleep Apnea, Obstructive
OSA; Prader-Willi Syndrome; orthognathic surgery
Xiao, K., Tomur, S., Beckerman, R., Cassidy, K., Lypka, M. Orthognathic Correction in Prader-Willi Syndrome: Occlusion and Sleep Restored. The Cleft palate-craniofacial journal : official publication of the American Cleft Palate-Craniofacial Association 56, 415-418 (2019).