Early childhood onset of high-grade atrioventricular block in Hunter syndrome.
Document Type
Article
Publication Date
5-2018
Identifier
DOI: 10.1017/S1047951118000215
Abstract
Cardiac involvement has been reported in various mucopolysaccharidoses syndromes. Cardiac valve pathology is the most prominent cardiac manifestation of patients with these syndromes. To date, there have been no reports of early childhood onset of high-grade atrioventricular block in patients with Hunter syndrome. We present a case of a 3-year-old boy with Hunter syndrome who was found to have various degrees of atrioventricular block. This case highlights the importance of early routine cardiac screening for conduction abnormalities and close follow-up in patients with mucopolysaccharidoses syndromes.
Journal Title
Cardiology in the young
Volume
28
Issue
5
First Page
786
Last Page
787
MeSH Keywords
Atrioventricular Block; Cardiac Pacing, Artificial; Child, Preschool; Electrocardiography; Follow-Up Studies; Humans; Male; Mucopolysaccharidosis II; Telemetry; Time Factors
Keywords
Children; Hunter syndrome; atrioventricular block; electrophysiology (EP)
Recommended Citation
Chlebowski MM, Heese BA, Malloy-Walton LE. Early childhood onset of high-grade atrioventricular block in Hunter syndrome. Cardiol Young. 2018;28(5):786-787. doi:10.1017/S1047951118000215