Considerations for Advanced Heart Failure Consultation in Individuals With Fontan Circulation: Recommendations From ACTION.

Document Type

Article

Publication Date

2-2023

Identifier

DOI: 10.1161/CIRCHEARTFAILURE.122.010123

Abstract

Individuals with Fontan circulation are at risk of late mortality from both cardiac and noncardiac causes. Despite the known risk of mortality, referral indications for advanced heart failure care vary between centers, and many individuals die from Fontan circulation-related complications either after late consideration for advanced heart failure therapies or having never seen a heart failure specialist. There is a critical need for guidelines to direct appropriately timed referral for advanced heart failure consultation. The Advanced Cardiac Therapies Improving Outcomes Network (ACTION) Fontan Committee has developed recommended thresholds for advanced heart failure referral to guide primary cardiologists. These recommendations are divided into 4 categories of clinical Fontan circulatory dysfunction including (1) cardiac/systemic ventricular dysfunction, (2) Fontan pathway dysfunction, (3) lymphatic dysfunction, and (4) extracardiac dysfunction.

Journal Title

Circ Heart Fail

Volume

16

Issue

2

First Page

010123

Last Page

010123

MeSH Keywords

Humans; Fontan Procedure; Heart Defects, Congenital; Heart Failure; Ventricular Dysfunction; Heart Ventricles

Keywords

Fontan procedure; congenital heart disease; heart failure; transplantation; ventricular dysfunction

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