Considerations for Advanced Heart Failure Consultation in Individuals With Fontan Circulation: Recommendations From ACTION.
Document Type
Article
Publication Date
2-2023
Identifier
DOI: 10.1161/CIRCHEARTFAILURE.122.010123
Abstract
Individuals with Fontan circulation are at risk of late mortality from both cardiac and noncardiac causes. Despite the known risk of mortality, referral indications for advanced heart failure care vary between centers, and many individuals die from Fontan circulation-related complications either after late consideration for advanced heart failure therapies or having never seen a heart failure specialist. There is a critical need for guidelines to direct appropriately timed referral for advanced heart failure consultation. The Advanced Cardiac Therapies Improving Outcomes Network (ACTION) Fontan Committee has developed recommended thresholds for advanced heart failure referral to guide primary cardiologists. These recommendations are divided into 4 categories of clinical Fontan circulatory dysfunction including (1) cardiac/systemic ventricular dysfunction, (2) Fontan pathway dysfunction, (3) lymphatic dysfunction, and (4) extracardiac dysfunction.
Journal Title
Circ Heart Fail
Volume
16
Issue
2
First Page
010123
Last Page
010123
MeSH Keywords
Humans; Fontan Procedure; Heart Defects, Congenital; Heart Failure; Ventricular Dysfunction; Heart Ventricles
Keywords
Fontan procedure; congenital heart disease; heart failure; transplantation; ventricular dysfunction
Recommended Citation
Lubert AM, Cedars A, Almond CS, et al. Considerations for Advanced Heart Failure Consultation in Individuals With Fontan Circulation: Recommendations From ACTION. Circ Heart Fail. 2023;16(2):e010123. doi:10.1161/CIRCHEARTFAILURE.122.010123