Creator(s)

John McDonnell
Kimberley Cousins
M Elizabeth M. Younger
Adam Lane
Hassan Abolhassani
Roshini S. Abraham
Salem Al-Tamemi
Juan Carlos Aldave-Becerra
Eman Hesham Al-Faris
Alberto Alfaro-Murillo
Suzan A. AlKhater
Nouf Alsaati
Alexa Michelle Altman Doss
Melissa Anderson, Children's Mercy Kansas City
Ernestina Angarola
Barbara Ariue
Danielle E. Arnold
Amal H. Assa'ad
Caner Aytekin
Meaghan Bank
Jenna R E Bergerson
Jack Bleesing
John Boesing
Carolina Bouso
Nicholas Brodszki
Diana Cabanillas
Carol Cady
Meghan A. Callahan
Roberta Caorsi
Javier Carbone
Maria Carrabba
Riccardo Castagnoli
Jason R. Catanzaro
Samantha Chan
Sharat Chandra
Hugo Chapdelaine
Zahra Chavoshzadeh
Hey Jin Chong
Lori Connors
Filippo Consonni
Oscar Correa-Jimenez
Charlotte Cunningham-Rundles
Katherine D'Astous-Gauthier
Ottavia Maria Delmonte
Yesim Yilmaz Demirdag
Deepti R. Deshpande
Natalie M. Diaz-Cabrera
Victoria R. Dimitriades
Rasha El-Owaidy
Gehad ElGhazali
Suleiman Al-Hammadi
Giovanna Fabio
Astrid Schellnast Faure
Jin Feng
James M. Fernandez
Lauren Fill
Guacira R. Franco
Robert W. Frenck
Ramsay L. Fuleihan
Giuliana Giardino
Jessica Galant-Swafford
Eleonora Gambineri
Elizabeth K. Garabedian
Ashley V. Geerlinks
Ekaterini Goudouris
Octavio Grecco
Qiang Pan-Hammarström
Hedieh Haji Khodaverdi Khani
Lennart Hammarström
Nicholas L. Hartog
Jennifer Heimall
Gabriela Hernandez-Molina
Caroline C. Horner
Robert W. Hostoffer
Nataliya Hristova
Kuang-Chih Hsiao
Gabriela Ivankovich-Escoto
Faris Jaber
Maaz Jalil
Mahnaz Jamee
Tiffany Jean
Stephanie Jeong
Devi Jhaveri
Michael B. Jordan
Avni Y. Joshi
Amanpreet Kalkat
Henry J. Kanarek
Erinn S. Kellner
Amer Khojah
Ruby Khoury
Cristina M. Kokron
Ashish Kumar
Kelsey Lecerf
Heather K. Lehman
Jennifer W. Leiding
Harry Lesmana
Xin Rong Lim
Joao Pedro Lopes
Ana Laura López
Lucia Tarquini
Ingrid S. Lundgren
Julieann Magnusson
Ana Karolina B B Marinho
Gian Luigi Marseglia
Giulia M. Martone
Annamaria G. Mechtler
Leonardo Mendonca
Joshua D. Milner
Peter J. Mustillo
Asal Gharib Naderi
Samuele Naviglio
Jeremy Nell
Hana B. Niebur
Luigi Notarangelo
Matias Oleastro
María Claudia Ortega-López
Neil R. Patel
Gordana Petrovic
Claudio Pignata
Oscar Porras
Benjamin T. Prince
Jennifer M. Puck
Nashmia Qamar
Marco Rabusin
Nikita Raje, Children's Mercy HospitalFollow
Lorena Regairaz
Kimberly A. Risma
Elizabeth H. Ristagno
John Routes
Persio Roxo-Junior
Negin Salemi
Christopher Scalchunes
Susan J. Schuval
Suranjith L. Seneviratne
Ashwin Shankar
Roya Sherkat
Junghee Jenny Shin
Abeer Siddiqi
Sara Signa
Ali Sobh
Fabiana Mascarenhas Souza Lima
Kristen K. Stenehjem
Jonathan S. Tam
Monica Tang
Myrthes Toledo Barros
James Verbsky
Eleni Vergadi
Dayne H. Voelker
Stefano Volpi
Luke A. Wall
Christine Wang
Kelli W. Williams
Eveline Y. Wu
Shan Shan Wu
Jessie J. Zhou
Alexandria Cook
Kathleen E. Sullivan
Rebecca Marsh

Document Type

Article

Publication Date

4-2024

Identifier

DOI: 10.1007/s10875-023-01613-5; PMCID: PMC10997719

Abstract

BACKGROUND: The CDC and ACIP recommend COVID-19 vaccination for patients with inborn errors of immunity (IEI). Not much is known about vaccine safety in IEI, and whether vaccination attenuates infection severity in IEI.

OBJECTIVE: To estimate COVID-19 vaccination safety and examine effect on outcomes in patients with IEI.

METHODS: We built a secure registry database in conjunction with the US Immunodeficiency Network to examine vaccination frequency and indicators of safety and effectiveness in IEI patients. The registry opened on January 1, 2022, and closed on August 19, 2022.

RESULTS: Physicians entered data on 1245 patients from 24 countries. The most common diagnoses were antibody deficiencies (63.7%). At least one COVID-19 vaccine was administered to 806 patients (64.7%), and 216 patients received vaccination prior to the development of COVID-19. The most common vaccines administered were mRNA-based (84.0%). Seventeen patients were reported to seek outpatient clinic or emergency room care for a vaccine-related complication, and one patient was hospitalized for symptomatic anemia. Eight hundred twenty-three patients (66.1%) experienced COVID-19 infection. Of these, 156 patients required hospitalization (19.0%), 47 required ICU care (5.7%), and 28 died (3.4%). Rates of hospitalization (9.3% versus 24.4%, p < 0.001), ICU admission (2.8% versus 7.6%, p = 0.013), and death (2.3% versus 4.3%, p = 0.202) in patients who had COVID-19 were lower in patients who received vaccination prior to infection. In adjusted logistic regression analysis, not having at least one COVID-19 vaccine significantly increased the odds of hospitalization and ICU admission.

CONCLUSION: Vaccination for COVID-19 in the IEI population appears safe and attenuates COVID-19 severity.

Journal Title

Journal of clinical immunology

Volume

44

Issue

4

First Page

86

Last Page

86

MeSH Keywords

Humans; COVID-19; COVID-19 Vaccines; Vaccination; Hospitalization; Critical Care

Keywords

Immunization; Immunodeficiency; Outcomes; Viruses: respiratory diseases

Comments

Grants and funding

This article is licensed under a Creative Commons Attribution 4.0 International License, which permits use, sharing, adaptation, distribution and reproduction in any medium or format, as long as you give appropriate credit to the original author(s) and the source, provide a link to the Creative Commons licence, and indicate if changes were made. The images or other third party material in this article are included in the article's Creative Commons licence, unless indicated otherwise in a credit line to the material. If material is not included in the article's Creative Commons licence and your intended use is not permitted by statutory regulation or exceeds the permitted use, you will need to obtain permission directly from the copyright holder. To view a copy of this licence, visit http://creativecommons.org/licenses/by/4.0/.

Publisher's Link: https://link.springer.com/article/10.1007/s10875-023-01613-5

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