Unilateral Facial Swelling in a Sickle Cell Patient.

Creator(s)

Rohan Akhouri, Children's Mercy HospitalFollow
Alison L. Fowler, Children's Mercy HospitalFollow
Colton Schwarz, Children's Mercy Kansas CityFollow
Lina Patel, Children's Mercy HospitalFollow

Document Type

Article

Publication Date

8-12-2024

Identifier

DOI: 10.7759/cureus.66693; PMCID: PMC11389757

Abstract

Acute soft head syndrome (ASHS) is a rare complication of sickle cell disease that often requires a high index of suspicion and is often a diagnosis of exclusion. We present the case of an 18-year-old male with sickle cell disease in the United States who developed acute soft head syndrome without known traumatic injury. The goal of this case presentation is to provide awareness and education regarding a rare complication of sickle cell disease and recommended management for the associated symptoms.

Journal Title

Cureus

Volume

16

Issue

8

First Page

66693

Last Page

66693

Keywords

acute soft head syndrome; facial swelling; hair-on-end appearance; pediatric emergency department; sickle cell complications

Recommended Citation

Akhouri R, Fowler A, Schwarz CT, Patel L. Unilateral Facial Swelling in a Sickle Cell Patient. Cureus. 2024;16(8):e66693. Published 2024 Aug 12. doi:10.7759/cureus.66693